The authors describe three cases of congenital monocular strabismus fixus with limited ocular motility in all directions. These were three boys aged two, two and 10 years. The right eye was affected in all with primary deviation angles of 30PD esotropia, no deviation and 100PD exotropia/50PD hypertropia respectively. MRI showed retrobulbar areas of low signal noise in the muscle cone in all cases, involving the extraocular muscles, posterior Tenon’s capsule and globe and could indicate fibrosis and adhesions. The authors decided, on these characteristics, that surgery would be ineffective and conclude that orbital imaging plays an important role in the diagnosis of these cases and the treatment plan decision making.